| 청각신경병증의 치료 |
| 정성욱, 김이석 |
| 동아대학교 의과대학 이비인후과학교실 |
| Management of Auditory Neuropathy
Spectrum Disorder |
| Sung Wook Jeong, Lee-Suk Kim |
| Department of Otolaryngology, Dong-A University College of Medicine, Busan, Korea |
| Correspondence |
Lee-Suk Kim ,Tel: +82-51-240-5428, Fax: +82-51-253-0712, Email: klsolkor@chol.com
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Received: February 21, 2016; Accepted: March 10, 2016. Published online: March 31, 2016. |
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| ABSTRACT |
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Auditory neuropathy spectrum disorder (ANSD) is a hearing disorder characterized by an absent or severely abnormal auditory brainstem
response (ABR) with preservation of cochlear microphonics or otoacoustic emissions (OAE). These findings suggest that outer hair cell is
normal but function of inner hair cell or auditory nerve is impaired. ANSD is a disorder in which behavioral threshold measures do not
match with other measures of auditory function such as ABR data and speech discrimination scores. The patients with ANSD can have
various hearing thresholds from normal to profound degree, but speech discrimination is very poor and out of proportion to pure tone
loss. Therefore conventional amplification is of little benefit to improve speech-language ability. Frequency-modulation system to enhance
signal-to-noise ratio can help in situations with background noise like classroom, car, and restaurant. Visual communication is also
helpful. Cochlear implantation is a promising tool for habilitation of patients with ANSD. Most patients who receive cochlear implantation
show significant improvements in speech perception abilities and good results in electrical ABR. However some very young children with
ANSD can recover during first 12-18 months of life and develop speech and language normally without any intervention. Therefore cochlear
implantation should be considered after the persistent ANSD is confirmed through repeated assessment using electrophysiological
measures and behavioral hearing tests. |
| Key Words:
Auditory neuropathy spectrum disorder, Cochlear implantation, Auditory brainstem response, Otoacoustic emission. |
| 중심단어:
청각신경병증· 인공와우이식· 청성뇌간반응· 이음향방사. |
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